Associated disease: Lupus-like syndrome; recurrent infections
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C1 (q,r,s)
Associated disease: Lupus-like syndrome; recurrent infections, ARTHEROSCLEROSIS
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C2
MOST COMMON complement deficiency.
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C2
Glomerulonephritis
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C3
MOST SEVERE complement deficiency.
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C3
Most commonly measure.
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C3
Lupus-like syndrome
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C4
Neisseria infections
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C5 - C7, Properdin
No known disease association.
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C9
Hereditary angioedema
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C1 - INH
Pneumococcal diseases, sepsis, neisseria infection
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MBL
Pneumococcal diseases, SEPSIS, Neisseria infection
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MASP 2
Recurrent pyogenic infections
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MBL
Paroxysmal nocturnal hemoglobinuria.
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DAF, MILRs