Disorders of the Airways

Question 1

Most fatal hereditary disorder of whites in the US

Answer 1

CF

Question 2

Symptoms include steatorrhea

Answer 2

CF

Question 3

How might your CF patient look?

Answer 3

Malnourished, digital clubbing, increased AP diameter

Question 4

What will you hear on lung exam in CF?

Answer 4

apical crackles

Question 5

What do PTF’s show in CF?

Answer 5

mixed obstructive and restrictive

Question 6

50% of CF patients will also develop this syndrome

Answer 6

bronchieactesis

Question 7

What abdominal organ are you also concerned with in CF?

Answer 7

pancreatits

Question 8

Symptoms of CF

Answer 8

productive cough, decreased exercise tolerance, recurrent hemoptysis, rhinosinusitis, diarrhea

Question 9

What is the tx of CF focused on?

Answer 9

reduction of airway secretions: postural drainage, chest percussion or vibration techniques

Question 10

What surgical intervention is available to CF patients?

Answer 10

lung transplant

Question 11

This disorder produces foul smelling sputum and can be congenital or acquired

Answer 11

bronchiectasis

Question 12

define bronchiectasis

Answer 12

abnormal, chronic bronchial enlargement; can be localized or diffuse

Question 13

Main symptoms of bronchieactasis

Answer 13

chronic cough with production of copious amounts of purulent sputum

Question 14

CXR findings of bronchieactasis

Answer 14

dilated and thickened bronchi–> “TRAM TRACKS”

Question 15

How do you treat bronchiectasis?

Answer 15

antibiotics for acute; usually amoxicillin

Question 16

What are some complications of bronchiectasis?

Answer 16

distant visceral abscesses–>brain! cor pulmonale, amyloidosis

Question 17

What is the hallmark symptom of interstitial lung disease ?

Answer 17

slowly progressing dyspnea (insidious onset) + dry cough

Question 18

What would lung volumes look like in a patient with interstitial lung disease?

Answer 18

decreased lung volumes w/ patchy distribution of ground glass

Question 19

What CXR findings would you expect to find in idiopathic interstitial pneumonia?

Answer 19

patchy, fibrosis honeycombing over several years

Question 20

What do PFT’s show in interstitial lung disease?

Answer 20

restrictive process

Question 21

How do you diagnosis idiopathic interstitial pneumonia?

Answer 21

surgical lung biopsy is usually required

Question 22

What are the four requirements for diagnosis idiopathic interstitial pneumonia?

Answer 22

honeycombing on CT over time
PTF’s with restrictive disease
inspiratory crackles
radiographic e/o fibrosis over years

Question 23

Who is at highest risk for developing sarcoidosis?

Answer 23

African American women

Question 24

noncaseating granulomas

Answer 24

sarcoidosis

Question 25

What would you expect to find on cxr for sarcoidosis?

Answer 25

butterfly sign–> hilar adenopathy

Question 26

What additional, regular exam do sarcoidosis patients require?

Answer 26

a regular eye exam

Question 27

What is a good treatment option for sarcoidosis?

Answer 27

prednisone