Juvenile Dermatomyositis Flashcards Preview

Nelson - Rheumatic Diseases of Childhood > Juvenile Dermatomyositis > Flashcards

Flashcards in Juvenile Dermatomyositis Deck (20):
1

MC inflammatory myositis in children

JDM

2

Rheuma: Proximal muscle weakness and a characteristic rash

JDM

3

JDM, T/F: History of infection is commonly reported

T, in the past 3 months

4

JDM: First symptom in 50% of cases

Rash

5

JDM, T/F: Rash appears concomitant with weakness in a vast majority

F, 25% of the time

6

Rheuma: Shawl sign

JDM, erythema over chest and neck from extreme photosensitivity to UV light

7

Rheuma: Heliotrope rash

JDM, Blue-violet discoloration of eyelids

8

Rheuma: Gottron papules

JDM

9

Bright pink or pale shiny thickened ATROPHIC plaques over the PIP and DIP and occasionally on other areas seen in JDM

Gottron papules

10

Rheuma: Mechanic's hand

JDM

11

Thickened erythema and scaly rash in children over the palms and soles along the flexor tendons

Mechanic's hand

12

Mechanic's hand is associated with what antibodies

Anti-Jo-1 antibodies

13

Rheuma: Gower sign

JDM

14

JDM, T/F: Muscle weakness is symmetric

T

15

JDM, T/F: Characterized by head lag in a child after infancy

T

16

Use of hands on thighs to stand from a sitting position

Gower's sign

17

Associated with long-standing JDM

1) Lipodystrophy 2) Calcinosis

18

JDM: Criteria for diagnosis

Characteristic rash (Heliotrope or Gottron) + at least 3 of the ff: 1) Muscle weakness (symmetric, proximal) 2) Muscle enzyme elevation (CK, AST, LDH, aldolase) 3) EMG changes (myopathy, denervation) 4) Muscle biopsy (necrosis, inflammation)

19

JDM that presents with classic rash but no apparent muscle weakness or inflammation

Amyopathic JDM

20

Mainstay of therapy in JDM

Corticosteroids