What is pleuropulmonary blastoma associated with?
multilocular cystic nephroma (10%)
UAC positiong?
High- T8-10
Low L3-5
Typical presentation fro congenital lobar emphysema?
Airspace opacity that typically resolves and then the same area of lung gets more lucent with likely mass effect
What is the only ring that goes between the trachea and esophagus?
pulmonary sling
Most common type of esophageal atresia?
N- type, proximal esophageal atresia with distal anastamosis between distal esophagus and trachea
UVC positioning?
goes from umbilical to portal to ductus venosus to the IVC
Should be between IVC and right atrium
Asymmetric subglottic narrowing?
hemangioma
Croup is symmetric
What is the PHACES syndrome?
Posterior fossa brain malformation Hemangiomas Arterial anomalites Coarctation of aorta Eye abnormalitites Subglottic hemangiomas
Congenital diaphragmatic hernia, Bochdalek hernia?
Bochdalek are in the Back
Which sequestration is more common in children?
Extralobar (has its own pleura)
Bronchopulmonary dysplasia is due to______ and presents after ______ weeks?
chronic ventilation, increased PEEP
4 weeks
What is associated with a mirror right aortic arch?
larger percentage of truncus patient’s have an mirror right aortic arch than TOF
but 90% of mirror right aortic arch patient’s have TOF
Kartageners?
Sinus disease, situs inversus, and primary ciliary dyskinesia
Which cardiac rings have posterior impressions on the esophagus?
Right arch with aberrant left subclavian
Left arch with aberrant right subclavian
Double aortic arch (will have bilateral lateral indentions as well)
Most common infectious agent in newborn with pneumonia?
Beta-hemolytic strep
Frequently has low lung volumes, granular opacites, and pleural effusion
Heterogenous enhancing solid mass invading the chest wall in pediatric population?
Askin Tumor-primitive neuroectodermal tumor of the chest wall
Types of truncus deformities?
Type I- main trunk produces aorta and MPA
Type II- the right and left PA have a common takeoff at the main trunk but there is no MPA
Type III- Right and left PA arise separately from posterior aspect of the ascending aorta
Type IV- Collateral vessels from the aorta form pulmonary circulation
SMA to the right of the SMV?
Malrotation
What are the two types of gastric volvulus?
Organoaxial - rotate around long axis, common in paraesophageal hernia
Mesenteroaxial- rotate around short axis
Windsock deformity?
duodenal web
Meckel’s Diverticulum arises from the?
omphalomesenteric duct
can have gastric or pancreatic tissue
Polysplenia is associated with more or fewer cardiac malformations than asplenia?
Fewer, polyspelnia has fewer cardiac malformations
Polysplenia- duplication of left side and vice versa
What is associated with hemangioendothelioma?
High output cardiac failure
Kasabach- Merritt Syndrome- destruction of platelets
What is heaptoblastoma associated with?
Beckwith-Weidemann
Wilms
Can have multiple masses with venous invasion, can have calcifications
AFP is elevated (can also have precocious puberty from making B-HCG)
DDX: mesenchymal hamartoma- AFP is negative, calcs are uncommon, and predominately cystic
